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Animal starch storage disease is any one of many inborn errors of metabolism that result from either enzyme defects that affect the processing of glycogen synthesis or breakdown inside muscles, liver, and more cell types.
There come nine diseases that are unremarkably considered to become animal starch storage diseases:
GSD nature and severity We: glucose-6-phosphatase deficiency, von Gierke's disease
GSD nature and severity II: acid maltase deficiency, Pompe's disease
GSD nature and severity III: glycogen debrancher deficiency, Cori's disease or Forbe's disease
GSD nature and severity IV: glycogen branching enzyme deficiency, Andersen disease
GSD nature and severity V: muscle glycogen phosphorylase deficiency, McArdle disease
GSD nature and severity VI: liver phosphorylase deficiency, Hers's disease
GSD nature and severity VII: muscle phosphofructokinase deficiency, Tarui's disease
GSD nature and severity IX: phosphorylase kinase deficiency
GSD nature and severity XI: glucose transporter deficiency, Fanconi-Bickel disease
GSD nature and severity 0: glycogen synthase deficiency
Although animal starch synthase deficiency doesn't effect within storage of more animal starch in a liver, these are typically classified using the GSDs bedrive these are an additional defect of animal starch storage & potty cause similar problems.
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